Journal Of Indian College Of Cardiology

CASE REPORT
Year
: 2019  |  Volume : 9  |  Issue : 3  |  Page : 169--170

Supraventricular tachycardia as presenting feature of Nevi, Atrial myxoma, Myxoid neurofibromatosis, and Ephelides Syndrome


Sonali Vadi1, Milan Mehta2 
1 Consultant-Intensivist, Intensive Care Unit, Kokilaben Dhirubhai Ambani Hospital and Medical Research Center, Mumbai, India
2 Clinical Cardiologist, Department of Cardiology, Sardar Patel Heart Institute, Ankleshwar, Gujarat, India

Correspondence Address:
Dr. Sonali Vadi
Kokilaben Dhirubhai Ambani Hospital and Medical Research Center, Mumbai - 400 053, Maharashtra
India

NAME composed of Nevi, Atrial myxoma, Myxoid neurofibromatosis, and Ephelides is a rare autosomal dominant syndrome with unknown prevalence. NAME syndrome has variable clinical manifestations, including skin pigmentation, neurofibromatosis, congestive cardiac failure, or even stroke as a result of tumor emboli. To the best of our knowledge, there are no prior published reports of supraventricular tachycardia as the initial presenting finding in a patient with NAME syndrome, a common arrhythmia signaling a rare syndrome. We describe a woman who presented with supraventricular tachycardia. Her thorough clinical examination with detailed workup revealed the features of NAME syndrome.


How to cite this article:
Vadi S, Mehta M. Supraventricular tachycardia as presenting feature of Nevi, Atrial myxoma, Myxoid neurofibromatosis, and Ephelides Syndrome.J Indian coll cardiol 2019;9:169-170


How to cite this URL:
Vadi S, Mehta M. Supraventricular tachycardia as presenting feature of Nevi, Atrial myxoma, Myxoid neurofibromatosis, and Ephelides Syndrome. J Indian coll cardiol [serial online] 2019 [cited 2020 Feb 24 ];9:169-170
Available from: http://www.joicc.org/article.asp?issn=1561-8811;year=2019;volume=9;issue=3;spage=169;epage=170;aulast=Vadi;type=0